第 04 章 免疫系统疾病
共 258 条，按编码升序。
- 4A01.0抗体缺陷为主的免疫缺陷Immunodeficiencies with predominantly antibody defects
- 4A01.00遗传性无丙种球蛋白血症伴B细胞的缺乏或极度减少Hereditary agammaglobulinaemia with profoundly reduced or absent B cells
- 4A01.01B细胞数量正常或降低的两种以上免疫球蛋白严重缺乏的免疫缺陷症Immunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes with normal or low numbers of B cells
- 4A01.02特定抗体缺乏伴免疫球蛋白浓度正常或B细胞数量正常Specific antibody deficiency with normal immunoglobulin concentrations or normal number of B cells
- 4A01.03婴儿期短暂性低丙球蛋白血症Transient hypogammaglobulinaemia of infancy
- 4A01.04伴同种型或轻链缺陷和B细胞数量正常的免疫缺陷Immunodeficiencies with isotype or light chain deficiencies with normal number of B cells
- 4A01.05伴血清IgG或IgA重度降低、IgM正常或升高和B细胞数量正常的免疫缺陷Immunodeficiencies with severe reduction in serum IgG or IgA with normal or elevated IgM and normal numbers of B-cells
- 4A01.0Y其他特指的抗体缺陷为主的免疫缺陷Other specified immunodeficiencies with predominantly antibody defects
- 4A01.0Z未特指的抗体缺陷为主的免疫缺陷Immunodeficiencies with predominantly antibody defects, unspecified
- 4A01.1联合免疫缺陷Combined immunodeficiencies
- 4A01.10严重联合免疫缺陷Severe combined immunodeficiencies
- 4A01.11主要组织相容性复合体I类缺陷Major histocompatibility complex class I deficiency
- 4A01.12主要组织相容性复合体II类缺陷Major histocompatibility complex class II deficiency
- 4A01.1Y其他特指的联合免疫缺陷Other specified combined immunodeficiencies
- 4A01.1Z联合免疫缺陷，未特指Combined immunodeficiencies, unspecified
- 4A01.2免疫失调性疾病Diseases of immune dysregulation
- 4A01.20免疫缺陷综合征伴色素减退Immune dysregulation syndromes with hypopigmentation
- 4A01.21自身免疫为主要表现的免疫失调综合征Immune dysregulation syndromes presenting primarily with autoimmunity
- 4A01.22淋巴细胞增生为主要表现的免疫失调综合征Immune dysregulation syndromes presenting primarily with lymphoproliferation
- 4A01.23原发性噬血细胞性淋巴组织细胞增多症Primary haemophagocytic lymphohistiocytosis