早发性阿尔茨海默病所致痴呆
Dementia due to Alzheimer disease with early onset
- 上级条目
- 6D80 阿尔茨海默病所致痴呆
- 层级
- 5 级
定义
阿尔茨海默病所致痴呆,症状在 65 岁之前出现。这种病相对罕见,占所有病例的 5%以下,可能由基因决定(常染色体显性阿尔茨海默病)。临床表现可能与晚发性病例相似,但认知障碍的进展可能更快。
Dementia due to Alzheimer disease in which symptoms emerge before the age of 65 years. It is relatively rare, representing less than 5% of all cases, and may be genetically determined (autosomal dominant Alzheimer disease). Clinical presentation may be similar to cases with later onset, but progression of cognitive deficits may be more rapid.
索引词 可用于检索该条目的同义词与别名
- 早发性阿尔茨海默病所致痴呆
- 早发性阿尔茨海默病痴呆
- 阿尔茨海默型早老性痴呆
- 早发性阿尔茨海默痴呆
- 2型阿尔茨海默病痴呆
- 早发性阿尔茨海默病痴呆
- 早发性阿尔采末病型痴呆,无并发症
- 原发性退行性阿尔茨海默型痴呆,早发性
- 原发性退行性阿尔茨海默型早老性痴呆,无并发症
- 早老性阿尔茨海默脑硬化
- 早发性阿尔采末病所致痴呆
- 阿尔采末型早老性痴呆
- 阿尔茨海默型早老性痴呆
- 早老性脑硬化 [possible translation]
- 早老性硬化 [possible translation]
- 早老性硬化
- 早老性脑硬化
- 常染色体显性遗传阿尔茨海默病痴呆,早老素1突变
- 常染色体显性遗传阿尔茨海默病痴呆,早老素2突变
- 常染色体显性遗传阿尔茨海默病痴呆,淀粉样前体蛋白突变
英文词条(15)
- Dementia due to Alzheimer disease with early onset
- Alzheimer disease dementia with early onset
- Alzheimer type presenile dementia
- dementia in Alzheimer disease type 2
- dementia in Alzheimer disease with early onset
- early onset Alzheimer dementia
- early onset Alzheimer type dementia, uncomplicated
- presenile Alzheimer brain sclerosis
- presenile brain sclerosis
- presenile sclerosis
- primary degenerative Alzheimer type dementia, early onset
- primary degenerative Alzheimer type dementia, presenile onset, uncomplicated
- Autosomal dominant Alzheimer disease dementia, mutation of presenilin 1
- Autosomal dominant Alzheimer disease dementia, mutation of presenilin 2
- Autosomal dominant Alzheimer disease dementia, mutation of amyloid precursor protein
编码备注 Coding note
这些分类不可用作主要编码。当需要标识分类于他处的疾病引起的痴呆时,可将这些编码作为补充或附加编码。 对于多种病因引起的痴呆,对所有适用的病因进行编码。
This category should never be used in primary tabulation. The codes are provided for use as supplementary or additional codes when it is desired to identify the presence of dementia in diseases classified elsewhere. When dementia is due to multiple aetiologies, code all that apply.
后组配轴 Postcoordination
后组配是在主干编码之后追加的可选扩展轴(如侧别、具体解剖部位、严重程度),用于把「部位 + 侧别 + 病程」等细节一次表达完整。只有标注「必填」的轴在组合编码时必须给出,其余可留空。
- 相关疾患associatedWith可选
- 严重程度hasSeverity可选
- 病因hasCausingCondition必填