BD93.0
原发性淋巴水肿
Primary lymphoedema
- 上级条目
- BD93 淋巴水肿
- 层级
- 4 级
定义
淋巴管发育不全引起的淋巴水肿
Lymphoedema as a result of lymphatic vessel hypoplasia
跨章引用 同一概念在其他章节另有编码
索引词 可用于检索该条目的同义词与别名
- 原发性淋巴水肿
- 先天性淋巴水肿 [possible translation]
- 先天性淋巴水肿
- 单纯原发性淋巴水肿
- 先天性原发性淋巴水肿
- Milroy病
- 遗传性淋巴水肿I型
- 围青春期原发性淋巴水肿
- Meige病
- 遗传性淋巴水肿II型
- 早发型淋巴水肿
- 梅热病
- 散发性迟发型原发性淋巴水肿
- 复杂性原发性淋巴水肿
- 淋巴水肿伴房间隔缺损及面部改变
- 淋巴水肿-双行睫综合征
- LDS[淋巴水肿双行睫综合征]
- Hennekam淋巴管扩张-淋巴水肿综合征
- Hennekam综合征
- 淋巴水肿-小头畸形-脉络膜视网膜病变综合征
- 耳聋-淋巴水肿-白血病综合征
- Emberger综合征
英文词条(20)
- Primary lymphoedema
- Congenital lymphoedema
- Simple primary lymphoedema
- Congenital primary lymphoedema
- Hereditary lymphoedema type I
- Milroy disease
- Peripubertal primary lymphoedema
- Hereditary lymphoedema type II
- Lymphoedema praecox
- Meige disease
- Sporadic late-onset primary lymphoedema
- Complex primary lymphoedema
- Lymphoedema with atrial septal defects and facial changes
- Lymphoedema-distichiasis syndrome
- LDS - [lymphoedema distichiasis syndrome]
- Hennekam lymphangiectasia-lymphoedema syndrome
- Hennekam syndrome
- Lymphoedema, microcephaly and chorioretinopathy syndrome
- Deafness, lymphoedema and leukaemia syndrome
- Emberger syndrome
后组配轴 Postcoordination
后组配是在主干编码之后追加的可选扩展轴(如侧别、具体解剖部位、严重程度),用于把「部位 + 侧别 + 病程」等细节一次表达完整。只有标注「必填」的轴在组合编码时必须给出,其余可留空。
- 具体解剖部位specificAnatomy可选