黄甲综合征

定义

黄甲综合征的特征是指甲发黄、营养不良、厚且生长缓慢，伴有淋巴水肿和呼吸系统受累。所描述的病例不到100例。淋巴水肿更常发生在下肢。它可以在出生时或生命后期出现。发病通常伴随甲异常的发生。患者通常患有慢性支气管炎，有时还患有慢性鼻窦炎、支气管扩张和复发性肺炎。他们也可表现为胸腔积液（30%的病例）和支气管高反应性。大多数病例是散发的。然而，也有描述过家族性病例。病因不明。

Yellow nail syndrome is characterised by yellow, dystrophic, thick and slowly growing nails, associated with lymphoedema and respiratory involvement. Less than 100 cases have been described. Lymphoedema occurs more often in the lower limbs. It can appear at birth or later in life. Onset generally follows the onset of ungual abnormalities. Patients usually suffer from chronic bronchitis and in some cases, from chronic sinusitis, bronchiectasia and recurring pneumonitis. They can also present with pleural effusion (30% of cases) and bronchial hyperreactivity. Most cases are sporadic. However, familial forms have been described. Aetiology is unknown.

黄甲综合征的特征是指甲发黄、萎缩、厚且生长缓慢，伴有淋巴水肿和呼吸系统受累。报道病例不到 100 例。淋巴水肿多发生于下肢。淋巴水肿可在出生时或出生后出现。发病通常在指甲异常之后。患者通常患有慢性支气管炎，有些还患有慢性鼻窦炎、支气管扩张和复发性肺炎。他们还可能出现胸腔积液（30% 的病例）和气道高反应性。大多数病例为散发性。但也有家族性病例。病因不明。水肿可逆，这表明淋巴功能紊乱为继发性。呼吸道症状和淋巴水肿需要特殊治疗。

索引词 可用于检索该条目的同义词与别名

• 黄甲综合征
• 遗传性淋巴水肿和黄甲