4A41.01
幼年型皮肌炎
Juvenile dermatomyositis
- 上级条目
- 4A41.0 皮肌炎
- 层级
- 5 级
定义
幼年皮肌炎是皮肌炎的早发形式,是一种全身性的自身免疫性肌肉炎症,其特点是近端肌无力、诱发性皮肤病变和全身性表现。
Juvenile dermatomyositis is the early-onset form of dermatomyositis, a systemic autoimmune inflammatory muscle disorder, characterised by proximal muscle weakness, evocative skin lesion, and systemic manifestations.
索引词 可用于检索该条目的同义词与别名
- 幼年型皮肌炎
- 儿童型皮肌炎 [possible translation]
- 儿童型皮肌炎
- 低肌病性幼年型皮肌炎
- 幼年型皮肌炎伴皮肤血管炎
- 幼年型皮肌炎伴脂肪营养不良
- 幼年型皮肌炎伴脂质营养不良
- 幼年型皮肌炎伴脂肪萎缩
- 幼年型皮肌炎伴心肌炎
- 幼年型皮肌炎伴坏死性皮肤血管炎
- 无肌病性幼年型皮肌炎
- 幼年型皮肌炎伴钙质沉积
- 幼年型皮肌炎伴皮下钙化
- 幼年型皮肌炎叠加非器官特异性系统性自身免疫病
- 幼年型肌炎
英文词条(11)
- Juvenile dermatomyositis
- childhood type dermatomyositis
- Hypomyopathic juvenile dermatomyositis
- Juvenile dermatomyositis with cutaneous vasculitis
- Juvenile dermatomyositis with lipodystrophy
- Juvenile dermatomyositis with myocarditis
- Juvenile dermatomyositis with necrotising cutaneous vasculitis
- Amyopathic juvenile dermatomyositis
- Juvenile dermatomyositis with calcinosis
- Juvenile dermatomyositis with overlap to nonorgan specific systemic autoimmune disorders
- Juvenile myositis
后组配轴 Postcoordination
后组配是在主干编码之后追加的可选扩展轴(如侧别、具体解剖部位、严重程度),用于把「部位 + 侧别 + 病程」等细节一次表达完整。只有标注「必填」的轴在组合编码时必须给出,其余可留空。
- 临床表现hasManifestation可选