ICD-11 编码查询_国际疾病分类第 11 版中文版_在线疾病编码检索工具
3A51.4

复合杂合子镰状细胞疾患伴危象

Compound heterozygous sickling disorders with crisis

上级条目
3A51 镰状细胞疾患或其他血红蛋白病
层级
4 级

定义

合并危象的杂合镰状细胞形成疾患可表现为急性胸部综合征、脾隔离症、溶血危象和疼痛。

Compound heterozygous sickling disorders with crisis may present with acute chest syndrome, splenic sequestration, haemolytic crisis, and pain.

索引词 可用于检索该条目的同义词与别名

  • 复合杂合子镰状细胞疾患伴危象
  • 镰状细胞Hb-C病伴危象
  • Hb S Hb C病伴危象 [possible translation]
  • Hb SC病伴危象 [possible translation]
  • Hb S Hb C病伴危象
  • Hb SC病伴危象
  • 镰状细胞Hb-C病伴危象伴急性胸部综合征
  • 镰状细胞Hb-C病伴危象伴脾隔离症
  • 镰状细胞Hb-C病伴危象伴发热
  • 镰状细胞地中海贫血伴危象
  • 镰状细胞β地中海贫血伴危象
  • 地中海贫血Hb S病 [possible translation]
  • 地中海贫血Hb S病伴危象 [possible translation]
  • 地中海贫血Hb S病
  • 地中海贫血Hb S病伴危象
  • 镰状细胞地中海贫血伴危象伴急性胸部综合征
  • 镰状细胞地中海贫血伴危象伴发热
  • 镰状细胞地中海贫血伴危象伴发热
  • 镰状细胞性地中海贫血伴血管闭塞性疼痛
英文词条(15)
  • Compound heterozygous sickling disorders with crisis
  • Sickle cell Hb-C disease with crisis
  • Hb S Hb C disease with crisis
  • Hb SC disease with crisis
  • Sickle cell Hb-C disease with crisis with acute chest syndrome
  • Sickle cell Hb-C disease with crisis with splenic sequestration
  • Sickle cell Hb-C disease with crisis with fever
  • Sickle cell thalassaemia with crisis
  • sickle-cell beta thalassaemia with crisis
  • thalassaemia Hb S disease
  • thalassaemia Hb S disease with crisis
  • Sickle cell thalassaemia with crisis with acute chest syndrome
  • Sickle cell thalassaemia with crisis with splenic sequestration
  • Sickle cell thalassaemia with crisis with fever
  • Sickle-cell thalassaemia with vaso-occlusive pain

后组配轴 Postcoordination

该条目未定义后组配轴,直接使用上面的编码即可。后组配是在主干编码之后追加侧别、具体解剖部位、严重程度、病因等细节的可选组合方式,不是必填项。