ICD-11 编码查询_国际疾病分类第 11 版中文版_在线疾病编码检索工具
8B60.6

单肢肌萎缩

Monomelic amyotrophy

上级条目
8B60 运动神经元病
层级
4 级

定义

局限于一上肢或下肢的萎缩和肌无力、在二十或三十多岁发病、男性居多,散发是MMA的特征。其他典型特征包括:由于前角细胞受累,隐匿性出现下运动神经元体征,缺乏上运动神经元体征,进展缓慢,几年内病情稳定,以及良性无症状病程。MMA在亚洲尤其流行,但在在全世界都会遇到。

Atrophy and weakness restricted to one upper or lower limb, onset in the second or third decade, male predominance, and sporadic occurrence are characteristic features of MMA. Other typical features include: insidious onset of lower motor neuron signs due to anterior horn cell involvement, absence of upper motor neuron signs, slow progression followed by stabilization within a few years,, and a benign symptomatic disease course. MMA is particularly prevalent in Asia although it is encountered worldwide.

索引词 可用于检索该条目的同义词与别名

  • 单肢肌萎缩
  • 上肢单肢肌萎缩
  • 平山病
  • 单侧上肢萎缩
  • Hirayama病
  • 下肢单肢肌萎缩
  • 单侧下肢萎缩
英文词条(4)
  • Monomelic amyotrophy
  • Monomelic amyotrophy of upper limb
  • Hirayama disease
  • Monomelic amyotrophy of lower limb

后组配轴 Postcoordination

后组配是在主干编码之后追加的可选扩展轴(如侧别、具体解剖部位、严重程度),用于把「部位 + 侧别 + 病程」等细节一次表达完整。只有标注「必填」的轴在组合编码时必须给出,其余可留空。

  • 临床表现hasManifestation可选