3B64.14
血栓性血小板减少性紫癜
Thrombotic thrombocytopenic purpura
- 上级条目
- 3B64.1 获得性血小板减少症
- 层级
- 5 级
定义
这种情况是特发性的。本病特点是血液凝固异常,导致全身小血管中形成广泛的微细血栓,造成血小板计数低。这种情况可能表现为癫痫发作、偏瘫、感觉异常、视觉障碍和失语或贫血。通过鉴定血栓确诊。
This condition is idiopathic. This condition is characterised by abnormality of blood coagulation causing extensive microscopic clots to form in the small blood vessels throughout the body resulting in low platelet count. This condition may present with seizures, hemiplegia, paresthesias, visual disturbance, and aphasia or anaemia. Confirmation is by identification of thromboses.
索引词 可用于检索该条目的同义词与别名
- 血栓性血小板减少性紫癜
- TTP[血栓性血小板减少性紫癜]
- Moschcowitz综合征
- Moschcowitz病
- 抗-ADAMTS 13抗体引起的获得性血栓性血小板减少性紫癜
- ADAMTS-13缺乏引起的先天性血栓性血小板减少性紫癜
- 先天性血小板减少性紫癜
- Upshaw-Schulman综合征
- 血栓性血小板减少性紫癜引起的肾小球疾患
- 血栓性血小板减少性紫癜,特指为难治性
英文词条(10)
- Thrombotic thrombocytopenic purpura
- Moschcowitz disease
- Moschcowitz syndrome
- TTP - [thrombotic thrombocytopenic purpura]
- Acquired thrombotic thrombocytopenic purpura due to anti-ADAMTS 13 antibodies
- Congenital thrombotic thrombocytopenic purpura due to ADAMTS-13 deficiency
- Upshaw-Schulman syndrome
- congenital thrombocytopaenic purpura
- Glomerular disorders in thrombotic thrombocytopenic purpura
- Thrombotic thrombocytopenic purpura specified as refractory
后组配轴 Postcoordination
该条目未定义后组配轴,直接使用上面的编码即可。后组配是在主干编码之后追加侧别、具体解剖部位、严重程度、病因等细节的可选组合方式,不是必填项。