气管支气管骨化病

定义

骨化性气管支气管病是一种原因不明的罕见疾病，在支气管镜检查中出现频率为0.4%，影响大气道。它的特点是出现多个与气管软骨相连的骨质和软骨质粘膜下结节。这种异常免受气管后膜壁不受影响。尽管有明显的影像学变化，但由于严重的气道梗阻不常见，所以病人很少出现症状。对于有症状的气道梗阻病人，可能需要进行线性气管成形术。

Tracheobronchopathia osteochondroplastica is a rare disorder of unknown cause, seen with a frequency of 0.4 percent at bronchoscopy, affecting the large airways. It is characterised by the development of multiple osseous and cartilaginous submucosal nodules connected to tracheal cartilage. The abnormality spares the posterior tracheal membranous wall. In spite of marked radiographic changes, patients are only rarely symptomatic since severe airway obstruction is unusual. Linear tracheoplasty may be required in patients with symptomatic airway obstruction.

索引词 可用于检索该条目的同义词与别名

• 气管支气管骨化病
• 骨化性气管支气管病