ICD-11 编码查询_国际疾病分类第 11 版中文版_在线疾病编码检索工具
3B15

遗传性凝血因子缺乏不伴出血倾向

Inherited coagulation factor deficiency without bleeding tendency

上级条目
先天性或体质性出血性情况
层级
5 级

定义

一种由遗传性突变引起的疾病,导致凝血因子水平下降。这种疾病特点是凝血因子水平下降而不导致出血增加。在血样中发现凝血因子水平下降确诊。

A disease caused by a genetically inherited mutation leading to decreased levels of coagulation factor. This disease is characterised by decreased levels of coagulation factor without leading to increased haemorrhaging. Confirmation is by identification of decreased levels of coagulation factor in a blood sample.

索引词 可用于检索该条目的同义词与别名

  • 遗传性凝血因子缺乏不伴出血倾向
  • 先天性前激肽释放酶缺乏
  • 先天性高分子量激肽原缺乏
  • 遗传性因子XII缺乏
  • 先天性Hageman因子缺乏
  • 哈格曼因子缺乏
  • 哈格曼因子缺陷
  • 哈格曼缺乏症
  • 先天性哈格曼因子缺乏
  • 哈格曼缺陷
  • 因子XII缺乏 [possible translation]
  • Hageman缺陷 [possible translation]
  • Hageman缺乏症 [possible translation]
  • Hageman因子缺陷 [possible translation]
  • Hageman因子缺乏 [possible translation]
  • 先天性因子XII缺乏 [possible translation]
  • 因子XII缺乏病 [possible translation]
  • 因子XII缺乏病
  • Hageman因子缺陷
  • Hageman缺陷
  • Hageman因子缺乏
  • 因子XII缺乏
  • 先天性因子XII缺乏
  • Hageman缺乏症
英文词条(12)
  • Inherited coagulation factor deficiency without bleeding tendency
  • Congenital prekallikrein deficiency
  • Congenital high-molecular-weight kininogen deficiency
  • Hereditary factor XII deficiency
  • Congenital Hageman factor deficiency
  • Deficiency of factor XII
  • Hageman defect
  • Hageman deficiency
  • Hageman factor defect
  • Hageman factor deficiency
  • congenital factor XII deficiency
  • factor XII deficiency disease

后组配轴 Postcoordination

该条目未定义后组配轴,直接使用上面的编码即可。后组配是在主干编码之后追加侧别、具体解剖部位、严重程度、病因等细节的可选组合方式,不是必填项。