LD24.22
家族性巨颌症
Cherubism
- 层级
- 5 级
定义
巨颌症是一种良性儿童纤维-骨性遗传性疾病,仅限于面部下半部、上颌骨,尤其是下颌骨,双侧无痛性颌骨肿胀(呈现所谓的天使样外观)伴多囊性骨肿瘤和眼睛向天的外观。有关部位的牙列异常:牙齿缺失、未长出、移位、牙根吸收和错牙合畸形常见。
Cherubism is a benign fibro-osseous hereditary disorder of childhood, limited to the lower half of the face, the maxilla and particularly the mandible, with bilateral painless swelling of jaws (giving the so-called cherubic look) associated with multicystic bone tumours and eyes-to-heaven appearance. Dentition is also abnormal at the sites concerned: tooth agenesis, noneruption, displacement, root resorption and malocclusions are common.
索引词 可用于检索该条目的同义词与别名
- 家族性巨颌症
英文词条(1)
- Cherubism
后组配轴 Postcoordination
该条目未定义后组配轴,直接使用上面的编码即可。后组配是在主干编码之后追加侧别、具体解剖部位、严重程度、病因等细节的可选组合方式,不是必填项。