特发性肺纤维化

定义

特发性肺纤维化（IPF）被定义为一种原因不明慢性、进行性纤维化间质性肺炎（肺炎）的特殊形式，主要发生于老年人，仅限于肺部，并与UIP的组织病理学和/或放射学模式有关。IPF的定义要求排除其他形式的间质性肺炎（肺炎），包括与环境暴露、药物治疗或系统性疾病相关的其他特发性间质性肺炎（肺炎）和间质性肺病（ILD）。

Idiopathic pulmonary fibrosis (IPF) is defined as a specific form of chronic, progressive fibrosing interstitial pneumonia (pneumonitis) of unknown cause, occurring primarily in older adults, limited to the lungs, and associated with the histopathologic and/or radiologic pattern of UIP (Usual Interstitial Pneumonia). The definition of IPF requires the exclusion of other forms of interstitial pneumonia (pneumonitis) including other idiopathic interstitial pneumonias (pneumonitis) and Interstitial Lung Disease (ILD) associated with environmental exposure, medication, or systemic disease.

索引词 可用于检索该条目的同义词与别名

• 特发性肺纤维化
• 纤维化肺病
• 纤维化肺炎
• 纤维化肺泡炎
• IPF[特发性肺纤维化]
• 间质性肺纤维化
• 特发性肺纤维化 [possible translation]
• 肺纤维化NOS [possible translation]
• 肺纤维化NOS
• 特发性肺纤维化