先天性主动脉瓣上狭窄
Congenital supravalvar aortic stenosis
- 层级
- 6 级
定义
一种先天性心血管畸形，在窦管结合部主动脉狭窄，可延伸至升主动脉。 附加信息：“先天性主动脉瓣上狭窄”被描述为三种形式：沙漏样畸形、纤维膜和弥漫性升主动脉狭窄。主动脉瓣上狭窄可累及冠状动脉开口，主动脉瓣叶可被拴住。由于压力升高，冠状动脉可变得迂曲和扩张，并早期动脉粥样硬化可随之发生。
A congenital cardiovascular malformation with narrowing of the aorta at the level of the sinotubular junction which may extend into the ascending aorta. Additional information: 'Congenital supravalvar aortic stenosis' is described as three forms: an hourglass deformity, a fibrous membrane, and a diffuse narrowing of the ascending aorta. Supravalvar aortic stenosis may involve the coronary artery ostia, and the aortic leaflets may be tethered. The coronary arteries can become tortuous and dilated due to elevated pressures and early atherosclerosis may ensue.
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索引词 可用于检索该条目的同义词与别名
- 先天性主动脉瓣上狭窄
- 先天性主动脉瓣上狭窄
- 先天性主动脉狭窄
- 先天性主动脉狭窄
- 先天性升主动脉狭窄
- 先天性升主动脉狭窄
- 先天性主动脉狭窄
- 先天性主动脉狭窄
- 先天性主动脉狭窄NOS
英文词条（9）
- Congenital supravalvar aortic stenosis
- congenital aortic stenosis NOS
- congenital aortic stricture
- congenital ascending aortic stenosis
- congenital ascending aortic stricture
- congenital narrowed aorta
- congenital stenosis of aorta
- congenital stricture of aorta
- congenital supravalvular aortic stenosis
后组配轴 Postcoordination
该条目未定义后组配轴，直接使用上面的编码即可。后组配是在主干编码之后追加侧别、具体解剖部位、严重程度、病因等细节的可选组合方式，不是必填项。