多囊肾发育不良
Multicystic renal dysplasia
- 上级条目
- LB30 肾结构发育异常
- 层级
- 5 级
定义
多囊性肾发育不良(Multicystic renal dysplasia),或称多囊性发育不良肾(MCDK),是一种先天性疾病,指胎儿期肾脏未能正常发育,而是形成了充满液体的囊肿,而非正常的肾组织。最常影响单侧肾脏,而另一侧健康的肾脏通常可以代偿其功能,且多通过产前超声检查发现。双侧MCDK(影响双肾)是一种非常严重的情况,肾衰竭风险高,通常难以长期存活。
Multicystic renal dysplasia, or multicystic dysplastic kidney (MCDK), is a congenital condition where a kidney fails to develop properly in the womb, becoming a non-functional collection of fluid-filled cysts instead of normal kidney tissue. It most often affects a single kidney, allowing the other healthy kidney to compensate for its function, and is usually discovered via prenatal ultrasound. Bilateral MCDK, affecting both kidneys, is a very serious condition with a high risk of kidney failure and is often incompatible with long-term survival.
索引词 可用于检索该条目的同义词与别名
- 多囊肾发育不良
- MCDK - [多囊性肾发育不良]
- 发育性多囊肾
- 多囊性肾发育不良
- 多发性先天性肾囊肿
- 单侧多囊性肾发育不良
- 单侧多囊性肾发育不良
- 双侧多囊性肾发育不良
英文词条(8)
- Multicystic renal dysplasia
- MCDK - [multicystic dysplastic kidney]
- developmental multicystic kidney
- multicystic dysplastic kidney
- multiple congenital cysts of kidney
- Multicystic renal dysplasia, unilateral
- Unilateral multicystic dysplastic kidney
- Multicystic renal dysplasia, bilateral
后组配轴 Postcoordination
后组配是在主干编码之后追加的可选扩展轴(如侧别、具体解剖部位、严重程度),用于把「部位 + 侧别 + 病程」等细节一次表达完整。只有标注「必填」的轴在组合编码时必须给出,其余可留空。
- 侧别laterality可选