弥漫性嗜酸性筋膜炎

定义

弥漫性嗜酸细胞性筋膜炎又称舒尔曼病/弥漫性筋膜炎，是一种罕见的特发性疾病，与皮肤硬化有关（橘皮征），通常发展迅速。它是一种真皮和皮下硬化症，与皮下脂肪小叶间隔、浅筋膜和周缘的纤维化增厚有关。通常需要对皮损进行全层切除活检，发现皮下筋膜的纤维化才能诊断。发病于不寻常的体力劳动和外伤之后，尤其是在男性。

Also called Shulman disease/diffuse fasciitis, diffuse eosinophilic fasciitis is a rare idiopathic disorder associated with induration of the skin (orange-peel sign) that generally develops rapidly. It is a dermal and hypodermal sclerosis associated with fibrotic thickening of the subcutaneous adipose lobular septa, superficial fascia, and perimysium. Full thickness excisional biopsy of skin lesions revealing fibrosis of the subcutaneous fascia is generally required for diagnosis. Onset follows unusual physical exertion and trauma, especially in males.

索引词 可用于检索该条目的同义词与别名

• 弥漫性嗜酸性筋膜炎
• 嗜酸性筋膜炎
• 筋膜炎伴嗜酸性粒细胞增多综合征
• Shulman综合征
• 舒尔曼综合征
• 弥漫性筋膜炎 [possible translation]
• 弥漫性筋膜炎