8D87.0
多系统萎缩
Multiple system atrophy
- 层级
- 4 级
定义
多系统萎缩（MSA）是一种罕见的神经退行性疾病，以帕金森病、小脑、自主神经（勃起功能障碍、膀胱功能障碍）、直立性低血压和锥体功能的多种组合为特征。该疾病属于α-突触核蛋白病，是一组以α-突触核蛋白在受累脑区聚集为特征的疾病。有两种不同类型的MSA-P（伴有帕金森病）和MSA-C（伴有小脑功能障碍）。
Multiple system atrophy (MSA) is a rare neurodegenerative disorder characterised by varied combinations of parkinsonian, cerebellar, autonomic (erectile dysfunction, bladder dysfunction, orthostatic hypotension) and pyramidal features. The disease belongs to the group of alpha-synucleinopathies, a group of diseases characterised by aggregation of alpha-synuclein in affected brain regions. There are two different types: MSA-P (with parkinsonism) and MSA-C (with cerebellar dysfunction).
子条目 共 4 条
后组配轴 Postcoordination
该条目未定义后组配轴，直接使用上面的编码即可。后组配是在主干编码之后追加侧别、具体解剖部位、严重程度、病因等细节的可选组合方式，不是必填项。