EK91.2
原发性皮肤浆细胞增多症
Primary cutaneous plasmacytosis
- 层级
- 4 级
定义
由浆细胞聚集体对皮肤局部或多灶性密集浸润引起的皮肤疾病。它可能与高浓度血清IgG4有关。典型表现为累及躯干和四肢的广泛红棕色丘疹、结节和色素硬斑，但也可表现为单个结节或斑块。大多数患有这种罕见皮肤病的患者都是东亚后裔。有进展为全身淋巴增生性恶性肿瘤的风险。
A skin disorder resulting from focal or multifocal dense infiltration of the skin by plasma cell aggregates. It may be associated with high levels of serum IgG4. It typically presents as widespread reddish-brown papules, nodules and pigmented indurated plaques involving the trunk and limbs but may present as a single nodule or plaque. The majority of patients with this uncommon skin disorder are of East Asian descent. There is a risk of progression to systemic lymphoproliferative malignancy.
索引词 可用于检索该条目的同义词与别名
- 原发性皮肤浆细胞增多症
- 原发性皮肤浆细胞瘤
英文词条（2）
- Primary cutaneous plasmacytosis
- Primary cutaneous plasmacytoma
后组配轴 Postcoordination
该条目未定义后组配轴，直接使用上面的编码即可。后组配是在主干编码之后追加侧别、具体解剖部位、严重程度、病因等细节的可选组合方式，不是必填项。