先天性肺动脉瓣下狭窄
Congenital subpulmonary stenosis
- 层级
- 6 级
定义
与支持肺动脉瓣流出道狭窄有关的先天性心血管畸形。 附加信息：瓣膜下（漏斗状）肺动脉狭窄是指紧靠肺动脉瓣正下方心室流出道的狭窄。该术语最好用于心室-动脉连接异常的情况，如心室双出口。虽然如果心室-动脉连接正常，瓣膜下肺动脉狭窄是右心室流出道梗阻的一种类型，但在这种情况下，应使用“先天性右心室流出道梗阻”。 瓣膜下肺动脉狭窄也是左心室流出道梗阻的一种类型，其原因是心室-动脉连接不一致；当梗阻仅在紧靠肺动脉瓣下方明显时，应使用这一术语，否则应使用 "先天性左心室流出道梗阻 "这一术语。
A congenital cardiovascular malformation associated with narrowing within the outflow tract supporting the pulmonary valve. Additional information: subvalvar (infundibular) pulmonary stenosis is a narrowing of the outflow tract of the ventricle immediately below the pulmonic valve. This term should preferably be used in the setting of abnormal ventriculo-arterial connections, such as double outlet ventricle. Although subvalvar pulmonary stenosis is a type of right ventricular outflow tract obstruction if the ventriculo-arterial connections are normal, in this setting 'Congenital right ventricular outflow tract obstruction' should be used. Subvalvar pulmonary stenosis is also a type of left ventricular outflow tract obstruction in the setting of discordant ventriculo-arterial connections; this term should be used when the obstruction is only apparent immediately below the pulmonary valve, otherwise the term 'Congenital left ventricular outflow tract obstruction' should be used
除外词 明确排除、需编到其他条目的情况
索引词 可用于检索该条目的同义词与别名
- 先天性肺动脉瓣下狭窄
- 肺动脉漏斗部狭窄
英文词条（2）
- Congenital subpulmonary stenosis
- infundibular pulmonary stenosis
后组配轴 Postcoordination
该条目未定义后组配轴，直接使用上面的编码即可。后组配是在主干编码之后追加侧别、具体解剖部位、严重程度、病因等细节的可选组合方式，不是必填项。