散发性淋巴管平滑肌瘤病

定义

这是一种罕见的肺部疾病，导致整个肺部、支气管、肺泡隔、血管周围间隙和淋巴管平滑肌生长紊乱（平滑肌瘤），导致小气道阻塞（导致肺囊肿形成和气胸）和淋巴管阻塞（导致乳糜性胸腔积液）。LAM以散发形式出现，仅影响女性，通常为育龄期；LAM也见于结节性硬化症患者。

This is a rare lung disease that results in a proliferation of disorderly smooth muscle growth (leiomyoma) throughout the lungs, in the bronchioles, alveolar septa, perivascular spaces, and lymphatics, resulting in the obstruction of small airways (leading to pulmonary cyst formation and pneumothorax) and lymphatics (leading to chylous pleural effusion). LAM occurs in a sporadic form, which affects only females, usually of childbearing age; LAM also occurs in patients who have tuberous sclerosis.

索引词 可用于检索该条目的同义词与别名

• 散发性淋巴管平滑肌瘤病