纤维素性纵隔炎

定义

纤维性纵隔炎，也称为硬化性纵隔炎或纵隔纤维化，是一种以纵隔过度纤维化反应为特征的疾病。它可导致气道、大血管和其他纵隔结构受损，其发病率与纤维化的位置和程度直接相关。最常见的原因是组织胞浆菌病，这是一种罕见的晚期并发症，但也可能与其他感染和系统性自身免疫性疾病有关，如白塞氏病、肉芽肿性多血管炎和腹膜后纤维化。

Fibrosing mediastinitis, also known as sclerosing mediastinitis or mediastinal fibrosis, is a disorder characterised by an excessive fibrotic reaction in the mediastinum. It can result in compromise of airways, great vessels, and other mediastinal structures, with morbidity directly related to the location and extent of fibrosis. The commonest cause is histoplasmosis, of which it is a rare late complication, but it may also occur in association with other infections and with systemic autoimmune disorders such as Behçet disease, granulomatosis with polyangiitis and retroperitoneal fibrosis.

索引词 可用于检索该条目的同义词与别名

• 纤维素性纵隔炎
• 纵隔纤维化
• 纤维性纵隔炎
• 特发性纵隔纤维化 [possible translation]
• 特发性纵隔纤维化
• 组织胞浆菌病相关性纤维性纵隔炎
• 组织胞浆菌病相关性纵隔纤维化纵隔炎
• 与系统性自身免疫性疾病有关的纤维性纵隔炎
• 特发性脐纤维化