4A00.1Y
其他特指的补体系统缺陷
Other specified defects in the complement system
- 上级条目
- 4A00.1 补体系统缺陷
- 层级
- 5 级
索引词 可用于检索该条目的同义词与别名
- 其他特指的补体系统缺陷
- 补体成分C3缺乏
- D因子缺乏引起的复发性奈瑟菌感染
- 补体成分C4b结合蛋白缺乏
- 伴CD46缺乏的免疫缺陷病
- 膜辅助因子蛋白缺乏
- 膜辅助蛋白缺乏
- 伴衰变加速因子缺乏的免疫缺陷病
- CHAPLE综合征
- 免疫缺陷,伴DAF[衰变加速因子]缺乏
- 伴CD55缺乏的免疫缺陷病
- 伴H因子异常的免疫缺陷病
- 伴I因子异常的免疫缺陷病
- 伴备解素缺乏的免疫缺陷病
- 伴CD59缺乏的免疫缺陷病
- 伴MASP-2缺乏的免疫缺陷病
- 甘露聚糖结合凝集素丝氨酸蛋白酶2缺乏
- 伴MBL[甘露聚糖结合凝集素]缺乏的免疫缺陷病
- MBP[甘露聚糖结合凝集素]缺乏症
- 甘露聚糖结合凝集素缺乏症
- 甘露糖结合蛋白缺乏
- 伴纤凝胶蛋白-3缺乏的免疫缺陷病
英文词条(21)
- Other specified defects in the complement system
- Complement component C3 deficiency
- Recurrent Neisseria infections due to factor D deficiency
- Complement component C4b-binding protein deficiency
- Immunodeficiency with CD46 deficiency
- Membrane cofactor protein deficiency
- Immunodeficiency with decay accelerating factor deficiency
- CHAPLE syndrome
- Immunodeficiency with CD55 deficiency
- Immunodeficiency with DAF - [decay accelerating factor] deficiency
- Immunodeficiency with factor H anomaly
- Immunodeficiency with factor I anomaly
- Immunodeficiency with properdin deficiency
- Immunodeficiency with CD59 deficiency
- Immunodeficiency with MASP-2 deficiency
- Mannan-binding lectin serine protease 2 deficiency
- Immunodeficiency with MBL - [mannan-binding lectin] deficiency
- MBP - [mannan-binding lectin] deficiency
- Mannan-binding lectin deficiency
- Mannose-binding protein deficiency
- Immunodeficiency with ficolin-3 deficiency
后组配轴 Postcoordination
该条目未定义后组配轴,直接使用上面的编码即可。后组配是在主干编码之后追加侧别、具体解剖部位、严重程度、病因等细节的可选组合方式,不是必填项。