掌跖脓疱病
Palmoplantar pustulosis
- 上级条目
- EA90.4 脓疱型银屑病
- 层级
- 6 级
定义
掌跖脓疱病(PPP)是一种慢性炎症性皮肤病,其特征是手掌和脚底长满无菌脓疱,数月或数年反复发作。患处往往发红并有鳞屑;可能形成疼痛性裂。它与吸烟密切相关。高达24%的患者与身体其他部位的银屑病有关,但其基因特征似乎与寻常型银屑病不同。白细胞介素-36受体基因多态性与泛发性脓疱型银屑病密切相关,并在少数PPP患者中发现。
Palmoplantar pustulosis (PPP) is a chronic inflammatory skin condition characterised by crops of sterile pustules on the palms and soles which erupt repeatedly over months or years. The affected areas tend to become red and scaly; cracks may form and these are often painful. It is strongly associated with smoking. It is associated with psoriasis elsewhere on the body in up to 24% of patients though appears to have a genetic profile distinct from psoriasis vulgaris. Interleukin-36 receptor gene polymorphisms are strongly associated with generalised pustular psoriasis and have been detected in a minority of patients with PPP.
包含词 该编码包含的临床情况,通常不作为独立编码
- 掌跖脓疱性银屑病
英文词条(1)
- Palmoplantar pustular psoriasis
索引词 可用于检索该条目的同义词与别名
- 掌跖脓疱病
- 掌跖脓疱型银屑病
- PPP[掌跖脓疱病]
- 掌跖脓疱性银屑病
- 掌跖脓疱病
- 脓疱性细菌疹 [possible translation]
- 脓疱性细菌疹
- 药物诱导掌跖脓疱病
- 药物诱导掌跖脓疱性银屑病
- 急性掌跖脓疱性银屑病
- 慢性掌跖脓疱性银屑病
英文词条(10)
- Palmoplantar pustulosis
- PPP - [palmoplantar pustulosis]
- Palmoplantar pustular psoriasis
- Pustular bacterid
- Pustular psoriasis of the palms and soles
- Pustulosis palmaris et plantaris
- Drug-induced palmoplantar pustulosis
- Drug-induced palmoplantar pustular psoriasis
- Acute palmoplantar pustular psoriasis
- Chronic palmoplantar pustular psoriasis
后组配轴 Postcoordination
后组配是在主干编码之后追加的可选扩展轴(如侧别、具体解剖部位、严重程度),用于把「部位 + 侧别 + 病程」等细节一次表达完整。只有标注「必填」的轴在组合编码时必须给出,其余可留空。
- 病程course可选