全身型幼年特发性关节炎
Juvenile systemic arthritis
- 上级条目
- FA24 幼年特发性关节炎
- 层级
- 5 级
定义
全身型幼年特发性关节炎占幼年特发性关节炎（JIA）病例的10-11%，以关节外表现（发热、皮肤发疹）的严重程度和性别比例相等为特征。发热高峰与短暂皮肤发疹和弥漫性红斑病或荨麻疹样病变有关。关节炎的存在对于诊断至关重要，但可能在病程后期出现。受累部位的数量可变（单、少或多关节炎），以几乎对称的方式影响大小关节。这种特征性诊断三联征也可能伴有腺病和肝脾肿大。可能存在内脏并发症（心包炎、胸腔积液或伴腹痛的浆液性腹膜炎）。
Systemic-onset juvenile idiopathic arthritis represents 10-11% of cases of juvenile idiopathic arthritis (JIA) and is marked by the severity of the extra-articular manifestations (fever, cutaneous eruptions) and by an equal sex ratio. Fever peaks are associated with transient cutaneous eruptions and diffuse erythematosis or urticarial-like lesions. The presence of arthritis is essential for diagnosis but may appear later in the disease course. The number of sites affected is variable (mono-, oligo- or polyarthritis) affecting both the small and large joints in a nearly symmetrical manner. This characteristic diagnostic triad may also be associated with an adenopathy and hepatosplenomegaly. Visceral complications (pericarditis, pleural effusion or serous peritonitis with abdominal pain) may be present.
索引词 可用于检索该条目的同义词与别名
- 全身型幼年特发性关节炎
- Still病
- 系统性幼年型类风湿性关节炎
- 斯蒂尔病
- 全身型幼年特发性关节炎伴巨噬细胞活化综合征
- 全身型幼年特发性关节炎，多部位
- 幼年特发性关节炎全身型，多部位
- 全身型幼年特发性关节炎，肩部
- 幼年特发性关节炎全身型，肩部
- 幼年特发性全身型关节炎，肩锁关节
- 幼年特发性全身型关节炎，盂肱关节
- 幼年特发性全身型关节炎，胸锁关节
- 全身型幼年特发性关节炎，上臂
- 幼年特发性关节炎全身型，上臂
- 全身型幼年特发性关节炎，肘关节
- 全身型幼年特发性关节炎，前臂
- 幼年特发性关节炎全身型，前臂
- 全身型幼年特发性关节炎，腕关节
- 幼年特发性关节炎全身型，腕关节
- 全身型幼年特发性关节炎，手
- 幼年特发性关节炎全身型，手
- 全身型幼年特发性关节炎，腕
- 全身型幼年特发性关节炎，指
- 全身型幼年特发性关节炎，掌
- 幼年特发性全身型关节炎，骨盆区或大腿
- 幼年特发性关节炎全身型，骨盆区或大腿
- 全身型幼年特发性关节炎，髋关节
- 全身型幼年特发性关节炎，小腿
- 幼年特发性关节炎全身型，小腿
- 全身型幼年特发性关节炎，膝关节
- 幼年特发性全身型关节炎，踝或足
- 幼年特发性全身型关节炎，踝或足
- 全身型幼年特发性关节炎，跖
- 全身型幼年特发性关节炎，跗
- 全身型幼年特发性关节炎，趾
- 全身型幼年特发性关节炎，踝关节
- 全身型幼年特发性关节炎，其他足关节
- 全身型幼年特发性关节炎，头部
- 全身型幼年特发性关节炎，颈部
- 全身型幼年特发性关节炎，脊椎
英文词条（38）
- Juvenile systemic arthritis
- Still disease
- Juvenile systemic onset arthritis complicated by macrophage activation syndrome
- Juvenile systemic arthritis, multiple sites
- juvenile arthritis with systemic onset, multiple sites
- Juvenile systemic arthritis, shoulder region
- juvenile arthritis with systemic onset, shoulder region
- Juvenile systemic arthritis, acromioclavicular joint
- Juvenile systemic arthritis, glenohumeral joint
- Juvenile systemic arthritis, sternoclavicular joint
- Juvenile systemic arthritis, upper arm
- juvenile arthritis with systemic onset, upper arm
- Juvenile systemic arthritis, elbow joint
- Juvenile systemic arthritis, forearm
- juvenile arthritis with systemic onset, forearm
- Juvenile systemic arthritis, wrist joint
- juvenile arthritis with systemic onset, wrist joint
- Juvenile systemic arthritis, hand
- juvenile arthritis with systemic onset, hand
- Juvenile systemic arthritis, carpus
- Juvenile systemic arthritis, fingers
- Juvenile systemic arthritis, metacarpus
- Juvenile systemic arthritis, pelvic region or thigh
- juvenile arthritis with systemic onset, pelvic region or thigh
- Juvenile systemic arthritis, hip joint
- Juvenile systemic arthritis, lower leg
- juvenile arthritis with systemic onset, lower leg
- Juvenile systemic arthritis, knee joint
- Juvenile systemic arthritis, ankle or foot
- juvenile arthritis with systemic onset, ankle or foot
- Juvenile systemic arthritis, metatarsus
- Juvenile systemic arthritis, tarsus
- Juvenile systemic arthritis, toes
- Juvenile systemic arthritis, ankle joint
- Juvenile systemic arthritis, other joints in foot
- Juvenile systemic arthritis, head
- Juvenile systemic arthritis, neck
- Juvenile systemic arthritis, vertebral column
后组配轴 Postcoordination
后组配是在主干编码之后追加的可选扩展轴（如侧别、具体解剖部位、严重程度），用于把「部位 + 侧别 + 病程」等细节一次表达完整。只有标注「必填」的轴在组合编码时必须给出，其余可留空。
- 具体解剖部位specificAnatomy可选
- 临床表现hasManifestation可选
- 病因hasCausingCondition必填