先天性肺气道畸形
Congenital pulmonary airway malformations
- 上级条目
- LA75 肺结构发育异常
- 层级
- 5 级
定义
产前支气管结构未能正常发育引起的一种疾病。本病在新生儿期可能表现为严重呼吸窘迫，后期可能出现急性呼吸窘迫或感染，也可能无症状。本病与其他病变和正常肺的区别在于粘膜息肉样突起、囊壁内平滑肌和弹性组织增多、囊性实质内软骨缺失、粘液分泌细胞和炎症消失。
A disease caused by failure of the bronchial structure to correctly develop during the antenatal period. This disease may present with severe respiratory distress in the newborn period, acute respiratory distress or infection later in life, or may be asymptomatic. This disease can be distinguished from other lesions and normal lung by polypoid projections of the mucosa, an increase in smooth muscle and elastic tissue within the cyst walls, an absence of cartilage in the cystic parenchyma, mucous secreting cells, and the absence of inflammation.
包含词 该编码包含的临床情况，通常不作为独立编码
- 先天性多发肺部囊性病变
- 先天性蜂窝肺
英文词条（2）
- Congenital honeycomb lung
- Congenital polycystic disease of lung
除外词 明确排除、需编到其他条目的情况
索引词 可用于检索该条目的同义词与别名
- 先天性肺气道畸形
- 先天性囊性肺病
- 先天性肺囊肿
- CCAM[先天性肺囊腺瘤畸形]
- 先天性肺囊腺瘤畸形
- 先天性肺囊肿
- 先天性蜂窝肺 [possible translation]
- 先天性多发肺部囊性病变 [possible translation]
- 先天性多发肺部囊性病变 [possible translation]
- 先天性多发支气管囊肿 [possible translation]
- 先天性多发肺部囊性病变
- 先天性多发肺部囊性病变
- 先天性多发支气管囊肿
- 先天性蜂窝肺
- 先天性肺气道畸形0型
- CPAM 0型[先天性肺气道畸形0型]
- 先天性肺气道畸形1型
- CPAM 1型[先天性肺气道畸形1型]
- 先天性肺气道畸形2型
- CPAM 2型[先天性肺气道畸形2型]
- 先天性肺气道畸形3型
- CPAM 3型[先天性肺气道畸形3型]
- 先天性肺气道畸形4型
- CPAM 4型[先天性肺气道畸形4型]
英文词条（20）
- Congenital pulmonary airway malformations
- CCAM - [Congenital cystic adenomatoid malformation]
- Congenital cystic adenomatoid malformation
- Congenital cystic disease of lung
- Congenital cystic lung
- Congenital honeycomb lung
- Congenital lung cyst
- Congenital polycystic disease of lung
- Congenital polycystic lung
- Multiple congenital bronchogenic cysts
- Congenital pulmonary airway malformation type 0
- CPAM type 0 - [Congenital pulmonary airway malformation type 0]
- Congenital pulmonary airway malformation type 1
- CPAM type 1 - [Congenital pulmonary airway malformation type 1]
- Congenital pulmonary airway malformation type 2
- CPAM type 2 - [Congenital pulmonary airway malformation type 2]
- Congenital pulmonary airway malformation type 3
- CPAM type 3 - [Congenital pulmonary airway malformation type 3]
- Congenital pulmonary airway malformation type 4
- CPAM type 4 - [Congenital pulmonary airway malformation type 4]
后组配轴 Postcoordination
后组配是在主干编码之后追加的可选扩展轴（如侧别、具体解剖部位、严重程度），用于把「部位 + 侧别 + 病程」等细节一次表达完整。只有标注「必填」的轴在组合编码时必须给出，其余可留空。
- 侧别laterality可选